Academic Journal

Molecular profiling of immunoglobulin heavy-chain gene rearrangements unveils new potential prognostic markers for multiple myeloma patients

Bibliographic Details
Title: Molecular profiling of immunoglobulin heavy-chain gene rearrangements unveils new potential prognostic markers for multiple myeloma patients
Authors: Alejandro Medina, Cristina Jiménez, M. Eugenia Sarasquete, Marcos González, M. Carmen Chillón, Ana Balanzategui, Isabel Prieto-Conde, María García-Álvarez, Noemí Puig, Verónica González-Calle, Miguel Alcoceba, Isabel Cuenca, Santiago Barrio, Fernando Escalante, Norma C. Gutiérrez, Mercedes Gironella, Miguel T. Hernández, Anna Sureda, Albert Oriol, Joan Bladé, Juan-José Lahuerta, Jesús F. San Miguel, María-Victoria Mateos, Joaquín Martínez-López, María-José Calasanz, Ramón García-Sanz
Contributors: Repositorio de Navarra, Instituto de Salud Carlos III, Ministerio de Economía y Competitividad (España), Fundación CRIS contra el Cáncer, Fundacion de la Sociedad Española de Hematología y Hemoterapia, Universidad de Salamanca, European Commission, Consejo Superior de Investigaciones Científicas [https://ror.org/02gfc7t72], Institut Català de la Salut, [Medina A, Jiménez C, Sarasquete ME, González M, Chillón MC, Balanzategui A] Hospital Universitario de Salamanca (HUSAL), IBSAL, IBMCC (USAL-CSIC), CIBERONC, Salamanca, Spain. [Gironella M] Vall d’Hebron Hospital Universitari, Barcelona, Spain, Vall d'Hebron Barcelona Hospital Campus
Source: Blood Cancer J
Blood Cancer Journal
r-IGTP. Repositorio Institucional de Producción Científica del Instituto de Investigación Germans Trias i Pujol
instname
Repositorio Institucional de la Consejería de Sanidad de la Comunidad de Madrid
Consejería de Sanidad de la Comunidad de Madrid
Dadun. Depósito Académico Digital de la Universidad de Navarra
Universidad de Navarra
Dipòsit Digital de la UB
Universidad de Barcelona
Articles publicats en revistes (Ciències Clíniques)
Digital.CSIC. Repositorio Institucional del CSIC
Consejo Superior de Investigaciones Científicas (CSIC)
Scientia
Scientia. Dipòsit d'Informació Digital del Departament de Salut
Institut de Recerca Germans Trias i Pujol (IGTP)
Publisher Information: Springer Science and Business Media LLC, 2020.
Publication Year: 2020
Subject Terms: Adult, Male, 0301 basic medicine, Cèl·lules B, Immunoglobulin Variable Region, PHENOMENA AND PROCESSES::Genetic Phenomena::Gene Expression Regulation::Gene Expression Regulation, Neoplastic, Article, ENFERMEDADES::neoplasias::neoplasias por tipo histológico::neoplasias de células plasmáticas::mieloma múltiple, 03 medical and health sciences, DISEASES::Neoplasms::Neoplasms by Histologic Type::Neoplasms, Plasma Cell::Multiple Myeloma, Multiple myeloma, Regulació genètica, Biomarkers, Tumor, Humans, Aged, Aged, 80 and over, Gene Rearrangement, B cells, 0303 health sciences, Gene Expression Profiling, Mieloma múltiple, Middle Aged, Prognosis, 3. Good health, Gene Expression Regulation, Neoplastic, FENÓMENOS Y PROCESOS::fenómenos genéticos::regulación de la expresión génica::regulación de la expresión génica neoplásica, Multigene Family, Female, Immunoglobulin Heavy Chains, Multiple Myeloma, Follow-Up Studies
Description: Multiple myeloma is a heterogeneous disease whose pathogenesis has not been completely elucidated. Although B-cell receptors play a crucial role in myeloma pathogenesis, the impact of clonal immunoglobulin heavy-chain features in the outcome has not been extensively explored. Here we present the characterization of complete heavy-chain gene rearrangements in 413 myeloma patients treated in Spanish trials, including 113 patients characterized by next-generation sequencing. Compared to the normal B-cell repertoire, gene selection was biased in myeloma, with significant overrepresentation ofIGHV3,IGHD2andIGHD3, as well asIGHJ4gene groups. Hypermutation was high in our patients (median: 8.8%). Interestingly, regarding patients who are not candidates for transplantation, a high hypermutation rate (≥7%) and the use ofIGHD2andIGHD3groups were associated with improved prognostic features and longer survival rates in the univariate analyses. Multivariate analysis revealed prolonged progression-free survival rates for patients usingIGHD2/IGHD3groups (HR: 0.552, 95% CI: 0.361−0.845,p = 0.006), as well as prolonged overall survival rates for patients with hypermutation ≥7% (HR: 0.291, 95% CI: 0.137−0.618,p = 0.001). Our results provide new insights into the molecular characterization of multiple myeloma, highlighting the need to evaluate some of these clonal rearrangement characteristics as new potential prognostic markers.
Document Type: Article
Other literature type
File Description: application/pdf
Language: English
ISSN: 2044-5385
DOI: 10.1038/s41408-020-0283-8
DOI: 10.13039/501100000780
DOI: 10.13039/501100003329
DOI: 10.13039/501100004587
Access URL: https://www.nature.com/articles/s41408-020-0283-8.pdf
https://pubmed.ncbi.nlm.nih.gov/32029700
https://fundanet.igtp.cat/Publicaciones/ProdCientif/PublicacionFrw.aspx?id=3999
https://hdl.handle.net/20.500.12530/61737
https://hdl.handle.net/10171/67156
http://hdl.handle.net/2445/173319
https://hdl.handle.net/2445/173319
http://hdl.handle.net/10261/222943
https://hdl.handle.net/11351/6280
http://digital.csic.es/bitstream/10261/222943/1/molecpatie.pdf
https://europepmc.org/article/MED/32029700
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7004993
http://diposit.ub.edu/dspace/bitstream/2445/173319/1/700354.pdf
https://www.nature.com/articles/s41408-020-0283-8
https://digital.csic.es/handle/10261/222943
Rights: CC BY
Accession Number: edsair.doi.dedup.....ab03ff8c3eb2bcb0bc89d89cd65a0f9b
Database: OpenAIRE
Description
ISSN:20445385
DOI:10.1038/s41408-020-0283-8