Academic Journal
Presentation of Sjogren Syndrome as Nodular Pulmonary Amyloidosis.
| Title: | Presentation of Sjogren Syndrome as Nodular Pulmonary Amyloidosis. |
|---|---|
| Authors: | Singh H; Internal Medicine, Henry Ford Health System, Jackson, USA., Patel PM; Internal Medicine, Henry Ford Health System, Jackson, USA., Ramanan S; Internal Medicine, Henry Ford Health System, Jackson, USA., Zebda H; Rheumatology, Henry Ford Health System, Detroit, USA., Malik D; Hematology/Oncology, Henry Ford Health System, Jackson, USA. |
| Source: | Cureus [Cureus] 2022 Oct 09; Vol. 14 (10), pp. e30103. Date of Electronic Publication: 2022 Oct 09 (Print Publication: 2022). |
| Publication Type: | Case Reports; Journal Article |
| Language: | English |
| Journal Info: | Publisher: Cureus, Inc Country of Publication: United States NLM ID: 101596737 Publication Model: eCollection Cited Medium: Print ISSN: 2168-8184 (Print) Linking ISSN: 21688184 NLM ISO Abbreviation: Cureus Subsets: PubMed not MEDLINE |
| Imprint Name(s): | Original Publication: Palo Alto, CA : Cureus, Inc. |
| Abstract: | Sjogren syndrome is an autoimmune disorder that leads to dryness in the eyes and mouth. Nodular pulmonary amyloidosis is a localized amyloid deposition pathology commonly seen with monoclonal lymphoproliferative disorders. We present a patient who came in with dyspnea and was found to have nodular pulmonary amyloidosis on biopsy. Commonly associated lymphoproliferative pathologies were ruled out and on further workup, the patient was found to have Sjogren syndrome. This case demonstrates pulmonary nodular amyloidosis as a rare presentation of Sjogren syndrome in the setting of relatively well-controlled symptoms. Detection of pulmonary nodular amyloidosis should prompt evaluation of associated conditions such as malignancy and autoimmune disorders to guide further management. (Copyright © 2022, Singh et al.) |
| Competing Interests: | The authors have declared that no competing interests exist. |
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| Contributed Indexing: | Keywords: amyloidosis; localized amyloid; pulmonary disease; pulmonary nodular amyloidosis; sjogren's disease |
| Entry Date(s): | Date Created: 20221116 Latest Revision: 20221117 |
| Update Code: | 20260130 |
| PubMed Central ID: | PMC9643031 |
| DOI: | 10.7759/cureus.30103 |
| PMID: | 36381813 |
| Database: | MEDLINE |
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