Εμφανίζονται 1 - 17 Αποτελέσματα από 17 για την αναζήτηση '"гипоплазия легких"', χρόνος αναζήτησης: 0,60δλ Περιορισμός αποτελεσμάτων
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    Academic Journal

    Πηγή: PAEDIATRIC SURGERY. UKRAINE; № 4(69) (2020): Paediatric Surgery. Ukraine; 13-23
    ХИРУРГИЯ ДЕТСКОГО ВОЗРАСТА; № 4(69) (2020): Хирургия детского возраста; 13-23
    Хірургія дитячого віку; № 4(69) (2020): Хірургія дитячого віку; 13-23

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    Academic Journal

    Πηγή: Tuberculosis, Lung Diseases, HIV Infection; № 4 (2019); 54-59
    Туберкулез, легочные болезни, ВИЧ-инфекция; № 4 (2019); 54-59
    Туберкульоз, легеневі хвороби, ВІЛ-інфекція; № 4 (2019); 54-59

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    Σύνδεσμος πρόσβασης: http://tubvil.com.ua/article/view/190334

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    Academic Journal

    Πηγή: Pediatric pharmacology; Том 17, № 6 (2020); 519-528 ; Педиатрическая фармакология; Том 17, № 6 (2020); 519-528 ; 2500-3089 ; 1727-5776

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    Relation: https://www.pedpharma.ru/jour/article/view/1923/1197; Whyte MP. Hypophosphatasia — aetiology, nosology, pathogenesis, diagnosis and treatment. Nat Rev Endocrinol. 2016;12(4):233–246. doi:10.1038/nrendo.2016.14.; Millán JL, Whyte MP. Alkaline phosphatase and hypophosphatasia. Calcif Tissue Int. 2016;98(4):398–416. doi:10.1007/s00223-015-0079-1.; Mornet E, Yvard A, Taillandier A, et al. A molecular-based estimation of the prevalence of hypophosphatasia in the European population. Ann Hum Genet. 2011;75(3):439–445. doi:10.1111/j.1469-1809.2011.00642.x.; Whyte MP, Leung E, Wilcox W, et al. Hypophosphatasia: a retrospective natural history study of the severe perinatal and infantile forms. Poster presented at the 2014 Pediatric Academic Societies and Asian Society for Pediatric Research Joint Meeting. Vancouver, B.C., Canada, May 5, 2014. Abstract 752416.; Whyte MP, Zhang F, Wenkert D, et al. Hypophosphatasia: validation and expansion of the clinical nosology for children from 25 years experience with 173 pediatric patients. Bone. 2015;75:229–239. doi:10.1016/j.bone.2015.02.022.; Bishop N, Munns CF, Ozono K. Transformative therapy in hypophosphatasia. Arch Dis Child. 2016;101(6):514–515. doi:10.1136/archdischild-2015-309579.; Anderson HC, Harmey D, Camacho NP, et al. Sustained osteomalacia of long bones despite major improvement in other hypophosphatasia-related mineral deficits in tissue nonspecific alkaline phosphatase/nucleotide pyrophosphatase phosphodiesterase 1 double-deficient mice. Am J Pathol. 2005;166(6):1711–1720. doi:10.1016/S0002-9440(10)62481-9.; Braunstein NА. Multiple fractures, pain, and severe disability in a patient with adult-onset hypophosphatasia. Bone Rep. 2016;4:1–4. doi:10.1016/j.bonr.2015.10.005.; Whyte M. Hypophosphatasia. In: Thakker RV, Whyte MP, Eisman J, Igarashi T, eds. Genetics of bone biology and skeletal disease. London: Academic Press; 2013. pp. 337–360.; Whyte MP, Greenberg CR, Salman NJ, et al. Enzyme-replacement therapy in life-threatening hypophosphatasia. N Engl J Med. 2012;366(10):904–913. doi:10.1056/NEJMoa1106173.; Kishnani PS, Rush ET, Arundel P, et al. Monitoring guidance for patients with hypophosphatasia treated with asfotase alfa. Mol genet metab. 2017;122(1–2):4–17. doi:10.1016/j.ymgme.2017.07.010.; Whyte MP, Coburn SP, Ryan LM, et al. Hypophosphatasia: Biochemical hallmarks validate the expanded pediatric clinical nosology. Bone. 2018;110:96–106. doi:10.1016/j.bone.2018.01.022.; Rush ET. Childhood hypophosphatasia: to treat or not to treat. Orphanet J Rare Dis. 2018;13(1):116. doi:10.1186/s13023-018-0866-7.; Simon S, Resch H, Klaushofer K, et al. Hypophosphatasia: From Diagnosis to Treatment. Curr Rheumatol Rep. 2018;20(11):69. doi:10.1007/s11926-018-0778-5.; Khan AA, Josse R, Kannu P, et al. Hypophosphatasia: Canadian update on diagnosis and management. Osteoporos Int. 2019;30(9):1713–1722. doi:10.1007/s00198-019-04921-y.; Mornet E. Hypophosphatasia. Metabolism. 2018;82:142–155. doi:10.1016/j.metabol.2017.08.013.; Briot K, Roux C. Adult hypophosphatasia. Arch Pediatr. 2017;24(5S2):5S71–5S73. doi:10.1007/s00198-015-3346-0.; https://www.pedpharma.ru/jour/article/view/1923

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    Academic Journal

    Πηγή: Hospital Surgery. Journal named by L.Ya. Kovalchuk; No. 4 (2018); 107-110 ; Госпитальная хирургия. Журнал имени Л.А. Ковальчука; № 4 (2018); 107-110 ; Шпитальна хірургія. Журнал імені Л. Я. Ковальчука; № 4 (2018); 107-110 ; 2414-4533 ; 1681-2778 ; 10.11603/2414-4533.2018.4

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    Academic Journal

    Πηγή: Pediatric pharmacology; Том 13, № 6 (2016); 539-543 ; Педиатрическая фармакология; Том 13, № 6 (2016); 539-543 ; 2500-3089 ; 1727-5776

    Περιγραφή αρχείου: application/pdf

    Relation: https://www.pedpharma.ru/jour/article/view/1476/864; Whyte MP. Hypophosphatasia — aetiology, nosology, pathogenesis, diagnosis and treatment. Nat Rev Endocrinol. 2016;12(4): 233–246. doi:10.1038/nrendo.2016.14.; Millan JL, Whyte MP. Alkaline phosphatase and hypophosphatasia. Calcif Tissue Int. 2016;98(4):398–416. doi:10.1007/s00223-015-0079-1.; Mornet E, Yvard A, Taillandier A, et al. A molecular-based estimation of the prevalence of hypophosphatasia in the European population. Ann Hum Genet. 2011;75(3):439–445. doi:10.1111/j.1469-1809.2011.00642.x.; Whyte MP, Leung E, Wilcox W, et al. Hypophosphatasia: a retrospective natural history study of the severe perinatal and infantile forms. Poster presented at the 2014 Pediatric Academic Societies and Asian Society for Pediatric Research Joint Meeting. Vancouver, B.C., Canada, May 5, 2014. Abstract 752416.; Whyte MP, Zhang F, Wenkert D, et al. Hypophosphatasia: validation and expansion of the clinical nosology for children from 25 years experience with 173 pediatric patients. Bone. 2015; 75:229–239. doi:10.1016/j.bone.2015.02.022.; Bishop N, Munns CF, Ozono K. Transformative therapy in hypophosphatasia. Arch Dis Child. 2016;101(6):514–515. doi:10.1136/archdischild-2015-309579.; Anderson HC, Harmey D, Camacho NP, et al. Sustained osteomalacia of long bones despite major improvement in other hypophosphatasia-related mineral deficits in tissue nonspecific alkaline phosphatase/nucleotide pyrophosphatase phosphodiesterase 1 double-deficient mice. Am J Pathol. 2005;166(6):1711–1720. doi:10.1016/S0002-9440(10)62481-9.; Braunstein NА. Multiple fractures, pain, and severe disability in a patient with adult-onset hypophosphatasia. Bone Rep. 2016;4: 1–4. doi:10.1016/j.bonr.2015.10.005.; Whyte M. Hypophosphatasia. In: Thakker RV, Whyte MP, Eisman J, Igarashi T, editors. Genetics of bone biology and skeletal disease. London: Academic Press; 2013. p. 337–360.; Whyte MP, Greenberg CR, Salman NJ, et al. Enzyme-replacement therapy in life-threatening hypophosphatasia. N Engl J Med. 2012;366(10):904–913. doi:10.1056/NEJMoa1106173.; https://www.pedpharma.ru/jour/article/view/1476

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    Academic Journal

    Πηγή: Medical Visualization; № 4 (2017); 132-142 ; Медицинская визуализация; № 4 (2017); 132-142 ; 2408-9516 ; 1607-0763

    Περιγραφή αρχείου: application/pdf

    Relation: https://medvis.vidar.ru/jour/article/view/457/421; Wenstrom K.D., Weiner C.P., Janson J.W. A five-year statewide experience with congenital diaphragmatic hernia. Am. J. Obstet Gynecol.1991; 165: 838–842.; Langham M.R.J., Kays D.W., Ledbetter D.J., Frentzen B., Sanford L.L., Richards D.S. Congenital diaphragmatic hernia. Epidemiology and outcome. Clin. Perinatol. 1996; 23: 671–688.; Neville H.L., Jaksic T., Wilson J.M., Lally P.A., Hardin W.D. Jr., Hirschl R.B., Lally K.P. Bilateral congenital diaphragmatic hernia. J. Pediatr. Surg. 2003; 38: 522– 524. DOI:10.1053/jpsu.2003.50092.; Jeanty C., Nien J.K., Espinoza J., Kusanovic J.P., Gonçalves L.F., Qureshi F., Jacques S., Lee W., Romero R. Pleural and pericardial effusion: a potential ultrasonographic marker for the prenatal differential diagnosis between congenital diaphragmatic eventration and congenital diaphragmatic hernia. Ultrasound Obstet. Gynecol. 2007; 29: 378–387. DOI:10.1002/uog.3958.; Keijzer R., Puri P. Congenital diaphragmatic hernia. Semin. Pediatr. Surg. 2010; 19: 180–185. DOI:10.1053/j.sempedsurg.2010.03.001; Щёголев А.И., Туманова У.Н., Ляпин В.М. Гипоплазия легких: причины развития и патологоанатомическая характеристика. Международный журнал прикладных и фундаментальных исследований. 2017; 4 (3): 530–534.; Gilbert-Barness E., Spicer D.E., Steffensen T.S. Handbook of Pediatric Autopsy Pathology. New York: Springer Science + Business Media, 2014.; Askenazi S.S., Perlman M. Pulmonary hypoplasia: lung weight and radial alveolar count as criteria of diagnosis. Arch. Dis. Child. 1979; 54: 614–618.; Wigglesworth J.S., Desai R., Guerrini P. Fetal lung hypoplasia: biochemical and structural variations and their possible significance. Arch. Dis. Child. 1981; 56: 606–615.; Emery J.L., Mithal A. The number of alveoli in the terminal respiratory unit of man during late intrauterine life and childhood. Arch. Dis. 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Regulation of alveologenesis: clinical implications of impaired growth. Pathology. 2008; 40: 124–140. DOI:10.1080/00313020701818981.; Демидов В.Н., Машинец Н.В., Подуровская Ю.Л., Буров А.А. Врожденная диафрагмальная грыжа плода – возможности ультразвуковой диагностики и прогнозирование постнатального исхода. Акушерство и гинекология. 2014; 4: 38–45.; Gallot D., Boda C., Ughetto S., Perthus I., Robert-Gnansia E., Francannet C., Laurichesse- Delmas H., Jani J., Coste K., Deprest J., Labbe A., Sapin V., Lemery D. Prenatal detection and outcome of congenital diaphragmatic hernia: a French registry-based study. Ultrasound Obstet. Gynecol. 2007; 29: 276–283. DOI:10.1002/uog.3863.; Машинец Н.В. Диафрагмальная грыжа плода (диагностика, лечение, постнатальные исходы). Акушерство и гинекология. 2016; 2: 20–27. DOI: http://dx.doi.org/10.18565/aig.2016.2.20-26.; Vintzileos A.M., Campbell W.A., Rodis J.F., Nochimson D.J., Pinette M.G., Petrikovsky B.M. Comparison of six different ultrasonographic methods for predicting lethal fetal pulmonary hypoplasia. Am. J. Obstet. Gynecol. 1989; 162: 606–612.; Peralta C.F., Cavoretto P., Csapo B., Vandecruys H., Nicolaides K.H. Assessment of lung area in normal fetuses at 12–32 weeks. Ultrasound Obstet. Gynecol. 2005; 26: 718–724. DOI:10.1002/uog.2651.; Yoshimura S., Masuzaki H., Gotoh H., Fukuda H., Ishimaru T. Ultrasonographic prediction of lethal pulmonary hypoplasia: comparison of eight different ultrasonographic parameters. Am. J. Obstet. Gynecol. 1996; 175: 477–483.; Metkus A.P., Filly R.A., Stringer M.D., Harrison M.R., Adzick N.S. Sonographic predictors of survival in fetal diaphragmatic hernia. J. Pediatr. Surg. 1996; 31: 148–151.; Jani J., Keller R.L., Benachi A., Nicolaides K.H., Favre R., Gratacos E., Laudy J., Eisenberg V., Eggink A., Vaast P., Deprest J., Antenatal-CDH-Registry Group. Prenatal prediction of survival in isolated left-sided diaphragmatic hernia. Ultrasound Obstet. Gynecol. 2006; 27: 18–22. DOI:10.1002/uog.2688.; Jani J.C., Peralta C.F.A., Nicolaides K.H. Lung-to-head ratio to unify the technique. Ultrasound Obstet. Gynecol. 2012; 39: 2-6. DOI:10.1002/uog.11065.; Kasprian G., Balassy C., Brugger P.C., Prayer D. MRI of normal and pathological fetal lung development. Eur. J. Radiol. 2006; 57: 261–270. DOI:10.1016/j.ejrad.2005.11.031.; Triebwasser J.E., Treadwell M.C. Prenatal prediction of pulmonary hypoplasia. Semin Fetal Neonatal Med. 2017; 15. DOI:10.1016/j.siny.2017.03.001.; Tanigaki S., Miyakoshi K., Tanaka M., Hattori Y., Matsumoto T., Ueno K., Uehara K., Nishimura O., Minegishi K., Ishimoto H., Shinmoto H., Ikeda K., Yoshimura Y. Pulmonary hypoplasia: prediction with use of ratio of MR imaging-measured fetal lung volume to US- estimated fetal body weight. Radiology. 2004; 232: 767–772. DOI:10.1148/radiol.2323030359.; Jani J., Cannie M., Sonigo P., Robert Y., Moreno O., Benachi A., Vaast P., Gratacos E., Nicolaides K.H., Deprest J. Value of prenatal magnetic resonance imaging in the prediction of postnatal outcome in fetuses with diaphragmatic hernia. Ultrasound Obstet. Gynecol. 2008; 32: 793–799. DOI:10.1002/uog.6234.; Thayyil S., Sebire N.J., Chitty L.S., Wade A., Chong W., Olsen O., Gunny R.S., Offiah A.C., Owens C.M., Saunders D.E., Scott R.J., Jones R., Norman W., Addison S., Bainbridge A., Cady E.B., Vita E.D., Robertson N.J., Taylor A.M., MARIAS collaborative group. Post-mortem MRI versus conventional autopsy in fetuses and children: a prospective validation study. Lancet. 2013; 382: 223–233. DOI:10.1016/S0140-6736(13)60134-8.; Туманова У.Н., Щёголев А.И. Посмертная магнитно-резонансная томография плодов и новорожденных. Медицинская визуализация. 2015; 5: 128–136.; Туманова У.Н., Щеголев А.И. Возможности и ограничения виртуальной аутопсии в неонатологии. REJR. 2017; 1: 20–33. DOI:10.21569/2222-7415-2017-7-1-20-33.; Туманова У.Н., Быченко В.Г., Ляпин В.М., Воево дин С.М., Щеголев А.И. Врожденная диафрагмальная грыжа у новорожденного: МРТ-патоморфологические сопоставления. Медицинская визуализация. 2014; 4: 72–83.; Arthurs O.J., Thayyil S., Olsen O.E., Addison S., Wade A., Jones R., Norman W., Scott R.J., Robertson N.J., Taylor A.M., Chitty L.S., Sebire N.J., Owens C.M. Magnetic Resonance Imaging Autopsy Study (MaRIAS) Collaborative Group. Diagnostic accuracy of post-mortem MRI for thoracic abnormalities in fetuses and children. Eur. Radiol. 2014; 24: 2876–2884. DOI:10.1007/s00330-014-3313-8.; Туманова У.Н., Ляпин В.М., Быченко В.Г., Щеголев А.И., Сухих Г.Т. Посмертная МРТ для диагностики врожденной пневмонии. Вестник Российского государственного медицинского университета. 2016; 4: 48–55.; Tumanova U.N., Lyapin V.M., Shchegolev A.I., Sukhikh G.T. The possibility of postmortem MRI in the diagnosis of congenital pneumonia. Virchows Arch. 2016; 469 (S1): S183.; Туманова У.Н., Ляпин В.М., Быченко В.Г., Воеводин С.М., Щеголев А.И. Способ посмертной диагностики врожденной пневмонии у новорожденного. Патент на изобретение RUS 2609462 16.02.2016.; Thayyil S., Schievanoa S., Robertson N.J., Jones R., Chitty L.S., Sebire N.J., Taylor A.M. MaRIAS (Magnetic Resonance Imaging Autopsy Study) Collaborative group. A semi- automated method for non-invasive internal organ weight estimation by post-mortem magnetic resonance imaging in fetuses, newborns and children. Eur. J. Radiol. 2009; 72: 321–326. DOI:10.1016/j.ejrad.2008.07.013.; https://medvis.vidar.ru/jour/article/view/457

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