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1Academic Journal
Authors: Karamova A.E., Aulova K.M., Chikin V.V., Kubanov А.A.
Contributors: The article is prepared and published as a part of the state task of State Research Center of Dermatovenereology and Cosmetology № 056-00003-24-02 for 2024 and the 2025–2026 planning periods “The development of a somatic cell based medicinal product for the treatment of patients with epidermolysis bullosa”., Рукопись подготовлена и опубликована в рамках выполнения государственного задания ФГБУ «ГНЦДК» Минздрава России № 056-00003-24-02 на 2024 г. и на плановый период 2025–2026 гг. «Разработка лекарственного препарата на основе соматических клеток для лечения больных врожденным буллезным эпидермолизом».
Source: Vestnik dermatologii i venerologii; Vol 100, No 5 (2024); 21-31 ; Вестник дерматологии и венерологии; Vol 100, No 5 (2024); 21-31 ; 2313-6294 ; 0042-4609 ; 10.25208/vdv.1005
Subject Terms: epidermolysis bullosa, skin substitutes, skin grafting, врожденный буллезный эпидермолиз, эквиваленты кожи, тканеинженерные конструкты кожи
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Relation: https://vestnikdv.ru/jour/article/view/16794/pdf; https://vestnikdv.ru/jour/article/view/16794/pdf_1; https://vestnikdv.ru/jour/article/view/16794/pdf_2; https://vestnikdv.ru/jour/article/downloadSuppFile/16794/158558; https://vestnikdv.ru/jour/article/downloadSuppFile/16794/158559; https://vestnikdv.ru/jour/article/downloadSuppFile/16794/158643; https://vestnikdv.ru/jour/article/downloadSuppFile/16794/159047; https://vestnikdv.ru/jour/article/view/16794
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2Academic Journal
Contributors: The manuscript was prepared and published as part of the fulfillment of the state task of the Federal State Budgetary Institution «GNCDC» of the Ministry of Health of the Russian Federation «Improvement of methods of therapy for patients with congenital epidermolysis bullosa based on restoration of expression of structural proteins of the skin» for 2021–2023., Рукопись подготовлена и опубликована в рамках выполнения государственного задания ФГБУ «ГНЦДК» Минздрава России «Совершенствование методов терапии больных врожденным буллезным эпидермолизом, основанных на восстановлении экспрессии структурных белков кожи» на 2021–2023 гг.
Source: Vestnik dermatologii i venerologii; Vol 100, No 1 (2024); 24-30 ; Вестник дерматологии и венерологии; Vol 100, No 1 (2024); 24-30 ; 2313-6294 ; 0042-4609 ; 10.25208/vdv.1001
Subject Terms: epidermolysis bullosa, collagen VII, gentamicin, nonsense mutations, COL7A1, врожденный буллезный эпидермолиз, коллаген VII типа, гентамицин, нонсенс-мутации
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Relation: https://vestnikdv.ru/jour/article/view/16737/pdf_1; https://vestnikdv.ru/jour/article/view/16737/pdf; https://vestnikdv.ru/jour/article/view/16737/pdf_2; https://vestnikdv.ru/jour/article/view/16737/pdf_3; https://vestnikdv.ru/jour/article/downloadSuppFile/16737/158051; https://vestnikdv.ru/jour/article/view/16737
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3Academic Journal
Source: Pediatric pharmacology; Том 19, № 6 (2022); 479-483 ; Педиатрическая фармакология; Том 19, № 6 (2022); 479-483 ; 2500-3089 ; 1727-5776
Subject Terms: клинический случай, dystrophic epidermolisys bullosa, epidermolysis bullosa, clinical case, дистрофический буллезный эпидермолиз, врожденный буллезный эпидермолиз, буллезный эпидермолиз
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Relation: https://www.pedpharma.ru/jour/article/view/2230/1449; Kim WB, Alavi A, Walsh S, et al. Epidermolysis bullosa pruriginosa: a systematic review exploring genotype-phenotype correlation. Am J Clin Dermatol. 2015;16(2):81–87. https://doi.org/10.1007/s40257-015-0119-7; Ghosh S, Chaudhuri S, Jain VK. Epidermolysis bullosa pruriginosa: a rare presentation with asymptomatic lesions. Indian J Dermatol Venereol Leprol. 2013;79(2):235–237. https://doi.org/110.4103/0378-6323.107645; Kim WB, Alavi A, Pope E, et al. Epidermolysis Bullosa Pruriginosa: Case Series and Review of the Literature. Int J Low Extrem Wounds. 2015;14(2):196–199. https://doi.org/10.1177/1534734615572469; Nakamura E, Majima Y, Hashizume H, et al. Dominant dystrophic epidermolysis bullosa pruriginosa with a COL7A1 exon 87 c.6898C>T mutation. Clin Exp Dermatol. 2019;44(1):82–84. https://doi.org/10.1111/ced.13715; Loh CC, Kim J, Su JC, et al. Development, reliability, and validity of a novel Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI). J Am Acad Dermatol. 2014;70(1):89–97.e1-e13. https://doi.org/10.1016/j.jaad.2013.09.041; Jain SV, Harris AG, Su JC, et al. The Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI): grading disease severity and assessing responsiveness to clinical change in epidermolysis bullosa. J Eur Acad Dermatol Venereol. 2017;31(4):692–698. https://doi.org/10.1111/jdv.13953; de Onis M, Onyango AW, Borghi E, et al. Development of a WHO growth reference for school-aged children and adolescents. Bull World Health Organ. 2007;85(9):660–667. https://doi.org/10.2471/blt.07.043497; Fine JD, Bruckner-Tuderman L, Eady RA, et al. Inherited epidermolysis bullosa: updated recommendations on diagnosis and classification. J Am Acad Dermatol. 2014;70(6):1103–1126. https://doi.org/10.1016/j.jaad.2014.01.903; Vivehanantha S, Carr RA, McGrath JA, et al. Epidermolysis bullosa pruriginosa: a case with prominent histopathologic inflammation. JAMA Dermatol. 2013;149(6):727–731. https://doi.org/10.1001/jamadermatol.2013.155; Banky JP, Sheridan AT, Storer EL, et al. Successful treatment of epidermolysis bullosa pruriginosa with topical tacrolimus. Arch Dermatol. 2004;140(7):794–796. https://doi.org/10.1001/archderm.140.7.794; Ferreira S, Azevedo A, Velho GC, et al. Epidermolysis Bullosa Pruriginosa successfully treated with concomitant topical and systemic agents. Australas J Dermatol. 2020;61(4):355–357. https://doi.org/10.1111/ajd.13342; Ertop P, Vural S, Gökpınar Ili E, et al. Promising effect of intravenous immunoglobulin therapy for epidermolysis bullosa pruriginosa. Int J Dermatol. 2020;59(7):851–855. https://doi.org/10.1111/ijd.14951; Zhou AG, Little AJ, Antaya RJ. Epidermolysis bullosa pruriginosa treated with dupilumab. Pediatr Dermatol. 2021;38(2):526–527. https://doi.org/10.1111/pde.14493; Shehadeh W, Sarig O, Bar J, et al. Treatment of epidermolysis bullosa pruriginosa-associated pruritus with dupilumab. Br J Dermatol. 2020;182(6):1495–1497. https://doi.org/10.1111/bjd.18855; Clawson RC, Duran SF, Pariser RJ. Epidermolysis bullosa pruriginosa responding to dupilumab. JAAD Case Rep. 2021;16:69–71. https://doi.org/10.1016/j.jdcr.2021.07.036; Jiang X, Wang H, Lee M, et al. Epidermolysis Bullosa Pruriginosa Treated With Baricitinib. JAMA Dermatol. 2021;157(10):1243–1244. https://doi.org/10.1001/jamadermatol.2021.3174; Chen KJ, Fang S, Ye Q, et al. Successful use of tofacitinib in epidermolysis bullosa pruriginosa. Clin Exp Dermatol. 2022;47(3):598–600. https://doi.org/10.1111/ced.14998; Kaushik A, Mahajan R, Karim A, et al. Successful use of cyclosporine in epidermolysis bullosa pruriginosa. Dermatol Ther. 2020;33(6):e14489. https://doi.org/10.1111/dth.14489; Takahashi T, Mizutani Y, Ito M, et al. Dystrophic epidermolysis bullosa pruriginosa successfully treated with immunosuppressants. J Dermatol. 2016;43(11):1391–1392. https://doi.org/10.1111/1346-8138.13406; Ranugha PS, Mohanan S, Chandrashekar L, et al. Epidermolysis bullosa pruriginosa showing good response to low-dose thalidomide — a report of two cases. Dermatol Ther. 2014;27(1):60–63. https://doi.org/10.1111/dth.12047; Pallesen KAU, Lindahl KH, Bygum A. Dominant Dystrophic Epidermolysis Bullosa Pruriginosa Responding to Naltrexone Treatment. Acta Derm Venereol. 2019;99(12):1195–1196. https://doi.org/10.2340/00015555-3304; Caroppo F, Milan E, Giulioni E, Belloni Fortina A. A case of dystrophic epidermolysis bullosa pruriginosa treated with dupilumab. J Eur Acad Dermatol Venereol. 2022;36(5):e365-e367. https://doi.org/10.1111/jdv.17887; https://www.pedpharma.ru/jour/article/view/2230
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4Academic Journal
Authors: Давлатова , Сохира, Абдурахманова , Ульяна, Лим , Максим
Source: International Journal of Scientific Pediatrics; Vol. 2 No. 2 (2023): February; 66-70 ; Международный журнал научной педиатрии; Том 2 № 2 (2023): Февраль; 66-70 ; Xalqaro ilmiy pediatriya jurnali; Nashr soni. 2 No. 2 (2023): Fevral; 66-70 ; 2181-2926
Subject Terms: врождённый буллёзный эпидермолиз, новорожденный ребёнок, поражение кожи и слизистых, генетический дефект, congenital bullous epidermolysis, newborn baby, skin and mucosa lesions, genetic defect
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Relation: https://ijsp.uz/index.php/journal/article/view/97/61; https://ijsp.uz/index.php/journal/article/view/97
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5Academic Journal
Source: Сборник статей
Subject Terms: CONGENITAL EPIDERMOLYSIS BULLOSA, GENODERMATOSIS, VESICULAR DERMATOSIS, ВРОЖДЕННЫЙ БУЛЛЕЗНЫЙ ЭПИДЕРМОЛИЗ, ГЕНОДЕРМАТОЗ, ПУЗЫРНЫЕ ДЕРМАТОЗЫ
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Relation: Актуальные вопросы современной медицинской науки и здравоохранения: материалы VII Международной научно-практической конференции молодых учёных и студентов, Екатеринбург, 17-18 мая 2022 г.; http://elib.usma.ru/handle/usma/7857
Availability: http://elib.usma.ru/handle/usma/7857
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6Academic Journal
Authors: Irina Yu. Pronina, Nikolay N. Murashkin, Svetlana G. Makarova, Marina G. Vershinina, Elena L. Semikina, Elena F. Mavrikidi, И. Ю. Пронина, Н. Н. Мурашкин, С. Г. Макарова, М. Г. Вершинина, Е. Л. Семикина, Е. Ф. Маврикиди
Contributors: The research was funded by charitable foundation “BELA. Butterfly Children”, Исследование выполнено при поддержке фонда «Дети-бабочки».
Source: Current Pediatrics; Том 21, № 1 (2022); 36-41 ; Вопросы современной педиатрии; Том 21, № 1 (2022); 36-41 ; 1682-5535 ; 1682-5527
Subject Terms: остеопороз, phosphorus, epidermolysis bullosa, vitamin D, osteocalcin, C-terminal telopeptide of type 1 collagen, bone remodelling, osteoporosis, фосфор, врожденный буллезный эпидермолиз, витамин D, остеокальцин, С-концевой телопептид коллагена I типа, костное ремоделирование
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Relation: https://vsp.spr-journal.ru/jour/article/view/2834/1147; Moretti L. Notarnicola A, Panella A, et al. Severe osteoporosis treated with teriparatide in a patient affected by recessive epidermolysis bullosa dystrophica. Osteoporos Int. 2011;22(3):1003–1006. doi: https://doi.org/10.1007/s00198-010-1278-2; Lipozencić J. News from the first regional symposium on hereditary epidermolysis bullosa, Mediterranean — central and eastern Europe. Acta Dermatovenerol Croat. 2009;17(2):147–148.; Mariath LM, Santin JT, Schuler-Faccini L, Kiszewski AE. Inherited epidermolysis bullosa: update on the clinical and genetic aspects. An Bras Dermatol. 2020;95(5):551–569. doi: https://doi.org/10.1016/j.abd.2020.05.001; Буллезный эпидермолиз: руководство для врачей / под ред. Н.Н. Мурашкина, Л.С. Намазовой-Барановой. — М.: ПедиатрЪ; 2019. — 444 с.; Ingen-Housz-Oro S, Blanchet-Bardon C, Vrillat M, Dubertret L. Vitamin and trace metal levels in recessive dystrophic epidermolysis bullosa. J Eur Acad Dermatol Venereol. 2004;18(6):649–653. doi: https://doi.org/10.1111/j.1468-3083.2004.01067.x; Bruckner AL, Bedocs LA, Keiser E, et al. Correlates of low bone mass in children with generalized forms of epidermolysis bullosa. J Am Acad Dermatol. 2011;65(5):1001–1009. doi: https://doi.org/10.1016/j.jaad.2010.08.028; Епишев Р.В. Нутритивная поддержка детей с врожденным буллезным эпидермолизом: дис. … канд. мед. наук. — М.; 2018.; Bardhan A, Bruckner-Tuderman L, Chapple I, et. al Epidermolysis bullosa. Nat Rev Dis Primers. 2020;6(1):78. doi: https://doi.org/10.1038/s41572-020-0210-0; Fine JD, Bruckner-Tuderman L, Eady RAJ, et al. Inherited epidermolysis bullosa: updated recommendations on diagnosis and classification. J Am Acad Dermatol. 2014;70(6):1103–1126. doi: https://doi.org/10.1016/j.jaad.2014.01.903; Gruskay DM. Nutritional management in the child with epidermolysis bullosa. Arch Dermatol. 1988;124(5):760–761.; Lechner-Gruskay D, Honig PJ, Pereira G, McKinney S. Nutri tional and metabolic profile of children with epidermolysis bullosa. Pediatr Dermatol. 1988;5(1):22–27. doi: https://doi.org/10.1111/j.1525-1470.1988.tb00879.x; Reyes ML, Cattani A, Gajardo H, et al. Bone metabolism in children with epidermolysis bullosa. J Pediatr. 2002;140(4): 467–469. doi: https://doi.org/10.1067/mpd.2002.123287; Martinez AE, Mellerio JE. Osteopenia and osteoporosis in epidermolysis bullosa. Dermatol Clin. 2010;28(2):353–355, xi. doi: https://doi.org/10.1016/j.det.2010.01.006; Fewtrell MS, Allgrove J, Gordon I, et al. Bone mineralization in children with epidermolysis bullosa. Br J Dermatol. 2006;154(5): 959–962. doi: https://doi.org/10.1111/j.1365-2133.2005.07123.x; Bachrach LK. Acquisition of optimal bone mass in childhood and adolescence. Trends Endocrinol Metab. 2001;12(1):22–28. doi: https://doi.org/10.1016/s1043-2760(00)00336-2; Daci E, Cromphaut S, Bouillon R. Mechanisms influencing bone metabolism in chronic illness. Horm Res. 2002;58(Suppl 1):44–51. doi: https://doi.org/10.1159/000064758; Pass C, MacRae VE, Ahmed SF, et al. Inflammatory cytokines and the GH-IGF-1 axis: novel actions on bone growth. Cell Biochem Funct. 2009;27(3):119–127. doi: https://doi.org/10.1002/cbf.1551; Viswanathan A, Sylvester F. Chronic inflammatory disease: effects on bone. Rev Endocr Metab Disord. 2008;9(2):107–122. doi: https://doi.org/10.1007/s11154-007-9070-0; MacRae VE, Wong SC, Farquharson C, et al. Cytokine actions in growth disorders associated with pediatric chronic inflammatory disease. Int J Mol Med. 2006;18(6):1011–1018. doi: https://doi.org/10.3892/ijmm.18.6.1011; Manolagas SC, Jilka RL. Bone marrow cytokines and bone remodeling. Emerging insights into the pathophysiology of osteoporosis. N Engl J Med. 1995;332(5):305–311. doi: https://doi.org/10.1056/NEJM199502023320506
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7Academic Journal
Authors: Maria A. Leonova, Nikolay N. Murashkin, Anton S. Dvornikov, Irina Yu. Pronina, М. А. Леонова, Н. Н. Мурашкин, А. С. Дворников, И. Ю. Пронина
Contributors: Not specified, Не указан
Source: Current Pediatrics; Том 21, № 5 (2022); 383-390 ; Вопросы современной педиатрии; Том 21, № 5 (2022); 383-390 ; 1682-5535 ; 1682-5527
Subject Terms: половое созревание, Kindler syndrome, congenital epidermolysis bullosa, kindlin-1, physical development, puberty, синдром Киндлер, врожденный буллезный эпидермолиз, киндлин-1, физическое развитие
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Relation: https://vsp.spr-journal.ru/jour/article/view/3034/1228; Has C, Bauer JW, Bodemer C, et al. Consensus reclassification of inherited epidermolysis bullosa and other disorders with skin fragility. Br J Dermatol. 2020;183(4):614–627. doi: https://doi.org/10.1111/bjd.18921; Кубанов А.А., Альбанова В.И., Карамова А.Э. и др. Распространенность врожденного буллезного эпидермолиза у населения Российской Федерации // Вестник дерматологии и венерологии. — 2015. — Т. 91. — № 3. — С. 21–30.; Буллезный эпидермолиз: руководство для врачей / под ред. Н.Н. Мурашкина, Л.С. Намазовой-Барановой. — М.: ПедиатрЪ; 2019. — 444 с.; Bardhan A, Bruckner-Tuderman L, Chapple ILC, et al. Epidermolysis bullosa. Nat Rev Dis Primers. 2020;6(1):78. doi: https://doi.org/10.1038/s41572-020-0210-0; Lai-Cheong JE, McGrath JA. Kindler syndrome. Dermatol Clin. 2010;28(1):119–124. doi: https://doi.org/10.1016/j.det.2009.10.013; Maier K, He Y, Esser PR, et al. Single amino acid deletion in kindlin-1 results in partial degradation which can be rescued by chaperone treatment. J Invest Dermatol. 2016;136(5):920–929. doi: https://doi.org/10.1016/j.jid.2015.12.039; Simon D. Puberty in chronically diseased patients. Horm Res. 2002;57(Suppl 2):53–56. doi: https://doi.org/10.1159/000058102; Loh CC, Kim J, Su JC, et al. Development, reliability, and validity of a novel Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI). J Am Acad Dermatol. 2014;70(1):89–97.e1–13. doi: https://doi.org/10.1016/j.jaad.2013.09.041; Jain SV, Harris AG, Su JC, et al. The Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI): grading disease severity and assessing responsiveness to clinical change in epidermolysis bullosa. J Eur Acad Dermatol Venereol. 2017;31(4):692–698. doi: https://doi.org/10.1111/jdv.13953; de Onis M, Onyango AW, Borghi E, et al. Development of a WHO growth reference for school-aged children and adolescents. Bull World Health Organ. 2007;85(9):660–667. doi: https://doi.org/10.2471/blt.07.043497; Sotos JF, Tokar NJ. Appraisal of testicular volumes: volumes matching ultrasound values referenced to stages of genital development. Int J Pediatr Endocrinol. 2017;2017:7. doi: https://doi.org/10.1186/s13633-017-0053-y; Marshall WA, Tanner JM. Variations in the pattern of pubertal changes in boys. Arch Dis Child. 1970;45(239):13–23. doi: https://doi.org/10.1136/adc.45.239.13; Wolf RM, Long D. Pubertal Development. Pediatr Rev. 2016; 37(7):292–300. doi: https://doi.org/10.1542/pir.2015-0065; Martinez AE, Allgrove J, Brain C. Growth and pubertal delay in patients with epidermolysis bullosa. Dermatol Clin. 2010;28(2): 357–359, xii. doi: https://doi.org/10.1016/j.det.2010.01.007
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8Academic Journal
Authors: Kubanov A.A., Chikin V.V., Karamova A.E., Monchakovskaya E.S.
Source: Vestnik dermatologii i venerologii; Vol 97, No 6 (2021); 6-19 ; Вестник дерматологии и венерологии; Vol 97, No 6 (2021); 6-19 ; 2313-6294 ; 0042-4609 ; 10.25208/vdv.976
Subject Terms: inherited epidermolysis bullosa, topical treatment, wound care, antiseptics, disinfectants, antibiotics and antimicrobial agents in dermatology, врожденный буллезный эпидермолиз, наружная терапия, препараты для лечения ран и язв, антисептики, дезинфицирующие средства, антибиотики, противомикробные средства
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9Academic Journal
Authors: Irina Yu. Pronina, Nikolay N. Murashkin, Svetlana G. Makarova, Elena L. Semikina, Dmitry S. Yasakov, Stepan G. Grigoriev, И. Ю. Пронина, Н. Н. Мурашкин, С. Г. Макарова, Е. Л. Семикина, Д. С. Ясаков, С. Г. Григорьев
Contributors: The study was funded by “BELA. Butterfly Children” foundation., Исследование осуществлено при финансовой поддержке Фонда «Дети-бабочки».
Source: Current Pediatrics; Том 20, № 5 (2021); 407-412 ; Вопросы современной педиатрии; Том 20, № 5 (2021); 407-412 ; 1682-5535 ; 1682-5527
Subject Terms: дети, insufficiency, deficiency, congenital epidermolysis bullosa, children, недостаточность, дефицит, врожденный буллезный эпидермолиз
File Description: application/pdf; application/vnd.openxmlformats-officedocument.wordprocessingml.document
Relation: https://vsp.spr-journal.ru/jour/article/view/2760/1101; https://vsp.spr-journal.ru/jour/article/view/2760/1105; Bardhan A, Bruckner-Tuderman L, Chapple I, et al. Epidermolysis bullosa. Nat Rev Dis Primers. 2020;6(1):78. doi:10.1038/s41572-020-0210-0; Буллезный эпидермолиз: руководство для врачей / под ред. Н.Н. Мурашкина, Л.С. Намазовой-Барановой. — М.: ПедиатрЪ; 2019. — 444 с.; Fine JD, Bruckner-Tuderman L, Eady RAJ, et al. Inherited epidermolysis bullosa: updated recommendations on diagnosis and classification. J Am Acad Dermatol. 2014;70(6):1103-1126. doi:10.1016/j.jaad.2014.01.903; Fine JD. Epidemiology of inherited epidermolysis bullosa based on incidence and prevalence estimates from the National Epidermolysis Bullosa Registry. JAMA Dermatol. 2016;152(11):1231-1238. doi:10.1001/jamadermatol.2016.2473; Has C, Bauer JW, Bodemer C, et al. Consensus reclassification of inherited epidermolysis bullosa and other disorders with skin fragility. Br J Dermatol. 2020;183(4):614-627. doi:10.1111/bjd.18921; Mariath LM, Santin JT, Schuler-Faccini L, Kiszewski AE. Inherited epidermolysis bullosa: update on the clinical and genetic aspects. An Bras Dermatol. 2020;95(5):551-569. doi:10.1016/j.abd.2020.05.001; Альбанова В.И., Смольянникова В.А., Гольченко В.А. Синдром Киндлер — редкий тип врожденного буллезного эпидермолиза // Вестник дерматологии и венерологии. — 2015. — № 4. — С. 95-104.; Fine JD, Mellerio JE. Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part I. Epithelial associated tissues. J Am Acad Dermatol. 2009;61(3):367-384. doi:10.1016/j.jaad.2009.03.052; Fine JD, Mellerio JE. Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part II. Other organs. J Am Acad Dermatol. 2009;61(3):387-402. doi:10.1016/j.jaad.2009.03.053; Мурашкин Н.Н., Макарова С.Г., Епишев Р.В. и др. Оценка нутритивного дисбаланса у детей с врожденным буллезным эпидермолизом // Кремлевская медицина. Клинический вестник. — 2018. — № 1. — С. 61-65.; Reyes ML, Cattani A, Gajardo H, et al. Bone metabolism in children with epidermolysis bullosa. J Pediatr. 2002;140(4):467-469. doi:10.1067/mpd.2002.123287; Salera S, Tadini G, Rossetti D, et al. A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management. Clin Nutr. 2020;39(2):343-352. doi:10.1016/j.clnu.2019.02.023; Institute of Medicine, Food and Nutrition Board. Dietary Reference Intakes for Calcium and Vitamin D. Washington, DC: National Academy Press; 2010.; Cranney C, Horsely T, O'Donnell S, et al. Effectiveness and safety of vitamin D. Evid Rep Technol Asses (Full Rep). 2007;(158):1-235.; Pludowski P, Holick MF, Pilz S, et al. Vitamin D effects on musculoskeletal health, immunity, autoimmunity, cardiovascular disease, cancer, fertility, pregnancy, dementia and mortality-a review of recent evidence. Autoimmun Rev. 2013;12(10):976-989. doi:10.1016/j.autrev.2013.02.004; Martinez AE, Mellerio JE. Osteopenia and osteoporosis in epidermolysis bullosa. Dermatol Clin. 2010;28(2):353-355. doi:10.1016/j.det.2010.01.006; Varki R, Sadowski S, Uitto J, Pfendner E. Epidermolysis bullosa. II. Type VII collagen mutations and phenotype-genotype correlations in the dystrophic subtypes. J Med Genet. 2007;44(3):181-192. doi:10.1136/jmg.2006.045302; Vahidnezhad H, Youssefian L, Zeinali S, et al. Dystrophic Epidermolysis Bullosa: COL7A1 Mutation Landscape in a Multi-Ethnic Cohort of 152 Extended Families with High Degree of Customary Consanguineous Marriages. J Invest Dermatol. 2017;137:660-669. doi:10.1016/j.jid.2016.10.023; Rodari G, Guez S, Manzoni F, et al. Birmingham epidermolysis severity score and vitamin D status are associated with low BMD in children with epidermolysis bullosa. Osteoporos Int. 2017;28(4):1385-1392. doi:10.1007/s00198-016-3883-1; Макарова С.Г., Намазова-Баранова Л.С., Мурашкин Н.Н. и др. Коррекция нутритивного статуса в комплексной терапии детей, страдающих дистрофической формой врожденного буллезного эпидермолиза диагностика в педиатрии // Педиатрическая фармакология. — 2016. — Т. 13. — № 6. — С. 577-587. doi:10.15690/pf.v13i6.1672; Reimer A, Hess M, Schwieger-Briel A, et al. Natural history of growth and anaemia in children with epidermolysis bullosa: a retrospective cohort study. Br J Dermatol. 2020;182(6):1437-1448. doi:10.1111/bjd.18475; Епишев Р.В. Нутритивная поддержка детей с врожденным буллезным эпидермолизом: дис. . канд. мед. наук. — М.; 2018.; Fine JD, Tamura T, Johnson L. Blood vitamin and trace metal levels in epidermolysis bullosa. Arch Dermatol. 1989;125:374-379.; Ingen-Housz-Oro S, Blanchet-Bardon C, Vrillat M, Dubertret L. Vitamin and trace metal levels in recessive dystrophic epidermolysis bullosa. J Eur Acad Dermatol Venereol. 2004;18(6):649-653. doi:10.1111/j.1468-3083.2004.01067.x; Петрушкина А.А., Пигарова Е.А., Рожинская Л.Я. Эпидемиология дефицита витамина D в Российской Федерации // Остеопороз и остеопатии. — 2018. — Т. 21. — № 3. — С. 15-20. doi:10.14341/osteo10038; Национальная программа «Недостаточность витамина D у детей и подростков Российской Федерации: современные подходы к коррекции». — М.: ПедиатрЪ; 2018. — 96 с.
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10Academic Journal
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11Academic Journal
Authors: Kubanov A.A., Karamova A.E., Monchakovskaya E.S.
Source: Vestnik dermatologii i venerologii; Vol 96, No 1 (2020); 10-17 ; Вестник дерматологии и венерологии; Vol 96, No 1 (2020); 10-17 ; 2313-6294 ; 0042-4609 ; 10.25208/vdv.961
Subject Terms: congenital epidermolysis bullosa, cell therapy, gene therapy, genome editing, viral vectors, врожденный буллезный эпидермолиз, клеточная терапия, генная терапия, редактирование генома, вирусные векторы
File Description: application/pdf
Relation: https://vestnikdv.ru/jour/article/view/551/1036; https://vestnikdv.ru/jour/article/view/551
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12Academic Journal
Authors: Nikolay N. Murashkin, Roman V. Epishev, Alexander I. Materikin, Eduard T. Ambarchian, Leonid A. Opryatin, Roman A. Ivanov, Н. Н. Мурашкин, Р. В. Епишев, А. И. Материкин, Э. Т. Амбарчян, Л. А. Опрятин, Р. А. Иванов
Contributors: Not specified, Не указан
Source: Current Pediatrics; Том 19, № 6 (2020); 420-431 ; Вопросы современной педиатрии; Том 19, № 6 (2020); 420-431 ; 1682-5535 ; 1682-5527
Subject Terms: дети, ulceration, erosion, skin barrier, epidermolysis bullosa, atopic dermatitis, psoriasis, palmar-plantar diseases, children, язва, эрозия, кожный барьер, врожденный буллезный эпидермолиз, атопический дерматит, псориаз, ладонно-подошвенные заболевания
File Description: application/pdf
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Prevalence of immune disease in patients with wounds presenting to a tertiary wound healing centre. Int Wound J. 2012:9(4):403–411. doi:10.1111/j.1742-481X.2011.00899.x.; Rekha PD, Rao SS, Sahana TG, Prabhu A. Diabetic wound management. Br J Community Nurs. 2018;23(Sup9):S16–S22. doi:10.12968/bjcn.2018.23.Sup9.S16.; Hart DW, Wolf SE, Chinkes DL, et al. Effects of early excision and aggressive enteral feeding on hypermetabolism, catabolism, and sepsis after severe burn. J Trauma. 2003;54(4):755–764. doi:10.1097/01.TA.0000060260.61478.A7.; Schultz GS, Sibbald RG, Falanga V, et al. Wound bed prepa ration: A systematic approach to wound management. Wound Repair Regen. 2003;11(Suppl 1):S1–S28. doi:10.1046/j.1524-475x.11.s2.1.x.; White R, Cutting KF. Modern exudate management: A review of wound treatments. World Wide Wounds. 2006. Available online: http://www.worldwidewounds.com/2006/september/White/Modern-Exudate-Mgt.html. Accessed on August 17, 2020.; Paul J. Characteristics of chronic wounds that itch. Adv Skin Wound Care. 2013;26:320–332. doi:10.1097/01.ASW.0000431203.64591.2f.; Zakhary SA. The Development and Content Validation of a Multidisciplinary, Evidence-based Wound Infection Prevention and Treatment Guideline. Ostomy Wound Manage. 2017;63(11):18–29.; Jones SA, Bowler PG, Walker M, Parsons D. Controlling wound bioburden with a novel silver-containing Hydrofiber® dressing. Wound Repair Regen. 2004;12(3):288–294. 10.1111/j.1067-1927.2004.012304.x.; Bowler PG. Wound pathophysiology, infection and therapeutic options. Ann Med. 2002;34(6):419–427. doi:10.1080/078538902321012360.; Gardner SE, Haleem A, Jao Y-L, et al. Cultures of diabetic foot ulcers without clinical signs of infection do not predict outcomes. Diabetes Care. 2014;37(10):2693–2701. doi:10.2337/dc14-0051.; International Wound Infection Institute (IWII). Wound Infection in Clinical Practice. Wounds International. November 11, 2016. Available online: https://www.woundsinternational.com/download/resource/6003. Accessed on August 17, 2020.; World Union of Wound Healing Societies (WUWHS), Florence Congress, Position Document. Management of Biofilm. Wounds International. September 23, 2016. Available online: https://www.woundsinternational.com/download/resource/5926. Accessed on August 17, 2020.; James GA, Swogger E, Wolcott R, et al. Biofilms in chronic wounds. Wound Repair Regen. 2008;16(1):37–44. doi:10.1111/j.1524-475X.2007.00321.x.; Круглова Л.С., Генслер Е.М. Атопический дерматит: новые горизонты терапии // Медицинский Алфавит. Дерматология. — 2019. — Т. 1. — № 7(382). — С. 29–32. doi:10.33667/2078-5631-2019-1-7(382)-29-32.; Greb JE, Goldminz AM, Elder JT, et al. Psoriasis. Nat Rev Dis Primers. 2016;2:16082. doi:10.1038/nrdp.2016.82.; Cai Y, Fleming C, Yan J. New insights of T cells in the pathogenesis of psoriasis. Cell Mol Immunol. 2012;9(4):302–309. doi:10.1038/cmi.2012.15.; Brunner PM, Guttman-Yassky E, Leung DYM. The immunology of atopic dermatitis and its reversibility with broad-spectrum and targeted therapies. J Allergy Clin Immunol. 2017;139(4S):S65–S76. doi:10.1016/j.jaci.2017.01.011.; Baharestani MM. Pressure ulcers in special populations: neonates and pediatrics. In: Baranoski S, Ayello E, eds. Wound Care Essentials: Practice Principles. 2nd ed. Philadelphia, PA: Lippincott Williams & Wilkins; 2007.; Suraseranivongse S, Kaosaard R, Intakong P. A comparison of postoperative pain scales in neonates. Br J Anaesth. 2006; 97(4):540–544. doi:10.1093/bja/ael184.; Irving V, Bethell E, Burton F. Neonatal wound care: minimizing trauma and pain. Wounds UK. 2006;2(1):33–41.; Baharestani MM, Pope E. Chronic wounds in neonates and children. In: Krasner D, Rodeheaver GT, Sibbald GT, eds. Chronic Wound Care: A Clinical Source Book for Healthcare Professionals. 4th ed. Malvern, PA: HMP Communications; 2007. pp. 679–693.; Hollinworth H, Collier M. Nurses’ views about pain and trauma at dressing changes: results of a national survey. J Wound Care. 2000;9(8):369–373. doi:10.12968/jowc.2000.9.8.26282.; White R. A Multinational survey of the assessment of pain when removing dressings. Wounds UK. 2008;4(1).; Schumann H, Beljan G, Hoping D, Bruckner-Tuderman L. Atraumatic dressings in fragile skin conditions: use of the soft silicone dressing (Mepilex) in hereditary and acquired bullous skin disease. Poster presentation. EWMA; 2005.; Butcher M, White R. Quantifying the financial impact of pain at dressing change. In: Upton D, ed. Psychological impact of pain in patients with wounds. Wounds UK; 2011. pp. 52–77.; Davies P, Rippon M. Evidence review: the clinical benefits of Safetac technology in wound care. J Wound Care. 2008;Suppl:3–31.; Jones J, Williams H. Wound management should not be a pain. Br J Community Nurs. 2017;22(Sup9):S38–S46. doi:10.12968/bjcn.2017.22.Sup9.S38.; Fauziyah H, Gayatri D. Pain, stress, and sleep quality in chronic wound patients. Enferm Clin. 2018;28(Suppl 1):176–179. doi:10.1016/S1130-8621(18)30062-7.; Morgan D. Wounds — what should a dressings formulary include? Hospital Pharmacist. 2002;9(9):262–266.; Edwards-Jones V. Antimicrobial and barrier effects of silver against methicillin-resistant. Staphylococcus aureus. J Wound Care. 2006;15(7):285–290. doi:10.12968/jowc.2006.15.7.26951.; Leaper DJ. Silver dressings: their role in wound management. Int Wound J. 2006;3(4):282–294. doi:10.1111/j.1742-481X.2006.00265.x.; Bjarnsholt T, Kirketerp-Moller K, Kristiansen S, et al. Silver against Pseudomonas aeruginosa biofilms. APMIS. 2007;115(8):921–928. doi:10.1111/j.1600-0463.2007.apm_646.x.; Castellano JJ, Shafii SM, Ko F, et al. Comparative evaluation of silvercontaining antimicrobial dressings and drugs. Int Wound J. 2007;4(2):114–122. doi:10.1111/j.1742-481X.2007.00316.x.; Cutting K, White R, Edmonds M. The safety and efficacy of dressings with silver — addressing clinical concerns. Int Wound J. 2007;4(2):177–184. doi:10.1111/j.1742-481X.2007.00338.x.; Barrett S. Mepilex® Ag: an antimicrobial, absorbent foam dressing with Safetac® technology. Br J Nurs. 2009;18(Sup7): S28–S36. doi:10.12968/bjon.2009.18.Sup7.45133.; Koerner S, Adams D. Use of a soft silicone silver transfer dressing (SSSTD) under compression may manage biofilm and exudate while promoting patient comfort. Poster presentation at the 47th Annual Conference of the Wound Ostomy and Continence Nurses Society, San Antonio, TX, US, 2015.; McCarty S, Davies P, Rippon M. Mepilex Border Ag: an in-market evaluation. Poster presentation at the Wounds UK Conference, Harrogate, UK, 2013.; Chadwick P, Taherinejad F, Hamberg K, et al. Clinical and scientific data on a silver-containing soft-silicone foam dressing: an overview. J Wound Care. 2009;18(11):486–490. doi:10.12968/jowc.2009.18.11.45001.; Bibic A, Hamberg K. Antimicrobial effect of a new silver-containing soft silicone exudate transfer dressing against common wound pathogens in vitro. Poster presentation at the Symposium on Advanced Wound Care and Wound Healing Society, Orlando, FL, US, 2014.; Werthen M, Taherinejad F, Gerner E. In vitro study of silvercontaining wound dressings — adhesion, fluid handling and antimicrobial effect. Poster presentation at the European Wound Management Association Conference, Vienna, Austria, 2012.; Lo SF, Chang CJ, Hu WY, et al. The effectiveness of silverreleasing dressings in the management of non-healing chronic wounds: a meta-analysis. J Clin Nurs. 2009;18(5):716–728. doi:10.1111/j.1365-2702.2008.02534.x.; Carter MJ, Tingley-Kelley K, Warriner RA III. Silver treatments and silver-impregnated dressings for the healing of leg wounds and ulcers: a systematic review and meta-analysis. J Am Acad Dermatol. 2010;63(4):668–679. doi:10.1016/j.jaad.2009.09.007.; Leaper D, Munter C, Meaume S, et al. The use of Biatain Ag in hard-to-heal venous leg ulcers: meta-analysis of randomised controlled trials. PLoS One. 2013;8(7):e67083. doi:10.1371/journal.pone.0067083.; Mellerio JE. Infection and colonization in epidermolysis bullosa. Dermatol Clin. 2010;28(2):267–269. doi:10.1016/j.det.2010.01.004.; Буллезный эпидермолиз: руководство для врачей / под ред. Н.Н. Мурашкина, Л.С. Намазовой-Барановой. — М.: ПедиатрЪ; 2019. — 444 с.; International Consensus. Appropriate Use of Silver Dressings in Wounds. An Expert Working Group Consensus. London: Wounds International; 2012. Available online: https://www.woundsinternational.com/download/resource/6010. Accessed on August 17, 2020.; Best Practice Statement. The use of topical antiseptic/antimicrobial agents in wound management. 2nd ed. Wounds UK; 2011.; Mir G. Diabetic foot ulcer healing with a silver dressing combined with soft silicone technology. Wounds International. 2013;4(3): 15–18. Available online: https://www.woundsinternational.com/download/resource/6828. Accessed on: August 17, 2020.; Barrows C. Enhancing patient outcomes — reducing the bottom line: the use of antimicrobial soft silicone foam dressing in home health. Home Healthc Nurse. 2009; 27(5): 279–284. doi:10.1097/01.nhh.0000356778.78126.4d.; Silverstein P, Heimbach D, Meites H, et al. An open, parallel, randomized, comparative, multicenter study to evaluate the costeffectiveness, performance, tolerance, and safety of a silver-containing soft silicone foam dressing (intervention) vs silver sulfadiazine cream. J Burn Care Res. 2011;32(6):617–626. doi:10.1097/BCR.0b013e318236fe31.; Schumann H, Apelqvist J, Schmidtchen, A et al. Open, noncomparative, multicentre investigation exploring the tolerance of an absorbent foam dressing containing silver used in chronic wounds. Poster presentation at the European Wound Management Association Conference, Glasgow, UK, 2007.; Kheng DE. Evaluation of Mepilex Ag, a silver impregnated soft silicone absorbent dressing in patients with critically colonized venous leg ulcers — 5 case reviews. Poster presentation at the 3rd Congress of the World Union of Wound Healing Societies, Toronto, Canada, 2008.; Tong JW. Case reports on the use of antimicrobial (silver impregnated) soft silicone foam dressing on infected diabetic foot ulcers. Int Wound J. 2009;6(4):275–284. doi:10.1111/j.1742-481X.2009.00610.x.; Bello YM, Falabella AF, Schachner LA. Management of epidermolysis bullosa in infants and children. Clin Dermatol. 2003;21(4): 278–282. doi:10.1016/s0738-081x(03)00050-6.; Denyer J. Management of severe blistering disorders. Semin Neonatol. 2000;5(4):321–324. doi:10.1053/siny.2000.0017.; Ly L, Su JC. Dressings used in epidermolysis bullosa blister wounds: a review. J Wound Care. 2008;17(11):482–492. doi:10.12968/jowc.2008.17.11.31476.; Meola S. Epydermolysis bullosa: a new technique for mask ventilation. Paediatr Anaesth. 2008;18(11):1109–1111. doi:10.1111/j.1460-9592.2008.02594.x.; Schober-Flores C. Epidermolysis bullosa. Wound care pearls for the non-infected and infected wound. J Dermatol Nurs Assoc. 2009;1(1); 21–28. doi:10.1097/JDN.0b013e3181977521.; Lara-Corrales I, Arbuckle A, Zarinehbaf S, Pope E. Principles of wound care in patients with epidermolysis bullosa. Pediatr Dermatol. 2010;27(3):229–237. doi:10.1111/j.1525-1470.2010.01086.x.; Denyer J, Foster L. Use of a transparent porous dressing coated on the wound contact side with soft silicone (Mepitel One) in the management of children with epidermolysis bullosa. Poster presentation at Wounds UK Conference, Harrogate, United Kingdom, 2010.; Waring M, Rippon M, Bielfeldt S, et al. Cell attachment to adhesive dressings: qualitative and quantitative analysis. Wounds UK. 2008;4(3):35–47.; Denyer J, Pillay E, Clapham J. Best practice guidelines for skin and wound care in epidermolysis bullosa. International Consensus. Wounds International; 2017.; Gotschall CS, Morrison MI, Eichelberger MR. Prospective, randomized study of the efficacy of Mepitel® on children with partialthickness scalds. J Burn Care Rehab. 1998;19(4):279–283. doi:10.1097/00004630-199807000-00002.; Barrett S. Management of traumatic wounds with Mepitel One: a case study evaluation. Poster presentation at Wounds UK Conference, Harrogate, United Kingdom, 2010.; Sanchez FJG. Evaluation; first experiences of a new one-sided selffixating wound contact layer. Poster presentation at the European Wound Management Association Conference, Geneva, Switzerland, 2010.; Acton C. Use of Mepitel One in conjunction with negative pressure wound therapy: a case study series. Poster presentation at Wounds UK conference, Harrogate, United Kingdom, 2010.; Collin O. Use of Mepitel One dressing following hand surgery: a case study series. Poster presentation at the Australian Wound Management Conference, Perth, Australia, 2010.; Whalley A. Case study evaluations of Mepitel One in the management of wounds of patients with diabetes. Poster presentation at Wounds UK Conference, Harrogate, United Kingdom, 2010.; Weidinger S, Novak N. Atopic dermatitis. Lancet. 2016; 387(10023):1109–1122. doi:10.1016/S0140-6736(15)00149-X.; Wollenberg A, Barbarot S, Bieber T, et al. Consensus-based European guidelines for treatment of atopic eczema (atopic dermatitis) in adults and children: part I. J Eur Acad Dermatol Venereol. 2018;32(5):657–682. doi:10.1111/jdv.14891.; He H, Koh MJ-A, Lee HY, Ang SB. Pilot study of a customized nanotextile wet garment treatment on moderate and severe atopic dermatitis: A randomized clinical trial. Pediatr Dermatol. 2020;37(1):52–57. doi:10.1111/pde.13981.; Cadmus SD, Sebastian KR, Warren D, et al. Efficacy and patient opinion of wet-wrap dressings using 0.1% triamcinolone acetonide ointment vs cream in the treatment of pediatric atopic dermatitis: A randomized split-body control study. Pediatr Dermatol. 2019;36(4):437–441. doi:10.1111/pde.13830.; Nicol NH, Boguniewicz M. Wet Wrap Therapy in Moderate to Severe Atopic Dermatitis. Immunol Allergy Clin North Am. 2017; 37(1):123–139. doi:10.1016/j.iac.2016.08.003.; Gonzalez-Lopez G, Ceballos-Rodriguez RM, Gonzalez-Lopez JJ. Efficacy and safety of wet wrap therapy for patients with atopic dermatitis: a systematic review and meta-analysis. Br J Dermatol. 2017;177(3):688–695. doi:10.1111/bjd.15165.; Eichenfield LF, Tom WL, Chamlin SL, et al. Guidelines of care for the management of atopic dermatitis: section 1. Diagnosis and assessment of atopic dermatitis. J Am Acad Dermatol. 2014; 70(2):338–351. doi:10.1016/j.jaad.2013.10.010.; Georgesen C, Wildman H, Wang X, Magro C. Pediatric pustular psoriasis responsive to cyclosporine bridged to etanercept: A treatment approach. Dermatol Online J. 2017;23(11):13030/qt9787b6c0.; Sociedade Brasileira de Dermatologia. Consenso Brasileiro de psoriase 2012. Guias de avaliacao e tratamento. Rio de Janeiro: Sociedade Brasileira de Dermatologia; 2012.; Rosenbach M, Hsu S, Korman NJ, et al. Treatment of erythrodermic psoriasis: from the medical board of the National Psoriasis Foundation. J Am Acad Dermatol. 2010;62(4):655–662. doi:10.1016/j.jaad.2009.05.048.; Andersen RM, Thyssen JP, Maibach HI. The role of wet wrap therapy in skin disorders — a literature review. Acta Derm Venereol. 2015;95(8):933–939. doi:10.2340/00015555-2134.; Devillers AC, Oranje AP. Efficacy and safety of wet-wrap dressings as an intervention treatment in children with severe and/ or refractory atopic dermatitis: a critical review of literature. Br J Dermatol. 2006;154(4):579–585. doi:10.1111/j.1365-2133.2006.07157.x.
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13Academic Journal
Authors: V. I. Albanova, M. A. Nefedova, E. S. Monchakovskaya, V. V. Chikin, V. A. Smolyannikova, A. E. Karamova
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 83-89 (2017)
Subject Terms: врожденный буллезный эпидермолиз, 03 medical and health sciences, рецессивный дистрофический буллезный эпидермолиз, 0302 clinical medicine, RL1-803, hereditary epidermolysis bullosa, squamous-cell carcinoma, recessive dystrophic epidermolysis bullosa, Dermatology, плоскоклеточный рак кожи, 3. Good health
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14Academic Journal
Authors: A. A. Kubanov, V. I. Albanova, V. V. Chikin, R. V. Yepishev
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 6, Pp 47-56 (2017)
Subject Terms: врожденный буллезный эпидермолиз, перевязочные средства, раневые повязки, генная терапия, заместительная белковая терапия, клеточная терапия, аллогенные фибробласты, стволовые клетки, hereditary epidermolysis bullosa, dressings, wound dressings, gene therapy, protein replacement therapy, cell therapy, allogenous fibroblasts, stem cells, Dermatology, RL1-803
File Description: electronic resource
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15Academic Journal
Authors: V. I. Albanova, V. A. Smolyannikova, V. A. Golchenko
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 4, Pp 95-104 (2017)
Subject Terms: синдром киндлер, киндлин-1, пойкилодермия, псевдосиндактилия, врожденный буллезный эпидермолиз, kindler syndrome, kindlin-1, poikiloderma, pseudosyndactyly, hereditary epidermolysis bullosa, Dermatology, RL1-803
File Description: electronic resource
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16Academic Journal
Authors: A. A. Kubanov, V. I. Albanova, A. E. Karamova, V. V. Chikin, L. YE. Melekhina, YE. V. Bogdanova
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 21-30 (2017)
Subject Terms: врожденный буллезный эпидермолиз, эпидемиология, распространенность·, hereditary epidermolysis bullosa, epidemiology, prevalence, Dermatology, RL1-803
File Description: electronic resource
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17Academic Journal
Authors: V. I. Albanova, V. V. Chikin, R. V. Epishev
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 53-59 (2017)
Subject Terms: врожденный буллезный эпидермолиз, трансмиссионная электронная микроскопия, иммунофлюоресцентное антигенное картирование, молекулярная диагностика, пренатальная диагностика, генетическое консультирование, hereditary epidermolysis bullosa, transmission electron microscopy, immunofluorescence antigen mapping, molecular diagnostics, prenatal diagnostics, genetic consulting, Dermatology, RL1-803
File Description: electronic resource
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18Academic Journal
Authors: A. E. Karamova, V. V. Chikin, V. I. Albanova, V. A. Smolyannikova, M. A. Nefedova, E. S. Monchakovskaya
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 83-89 (2017)
Subject Terms: врожденный буллезный эпидермолиз, рецессивный дистрофический буллезный эпидермолиз, плоскоклеточный рак кожи, hereditary epidermolysis bullosa, recessive dystrophic epidermolysis bullosa, squamous-cell carcinoma, Dermatology, RL1-803
File Description: electronic resource
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19Academic Journal
Authors: V. I. Albanova, A. E. Karamova, V. V. Chikin, A. A. Mineyeva
Source: Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 46-53 (2017)
Subject Terms: дистрофический врожденный буллезный эпидермолиз, терапия, аллогенные фибробласты, recessive dystrophic epidermolysis bullosa, therapy, allogeneic fibroblasts, Dermatology, RL1-803
File Description: electronic resource
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20Academic Journal
Authors: Kubanov A.A., Karamova A.E., Albanova V.I., Monchakovskaya E.S.
Source: Vestnik dermatologii i venerologii; Vol 95, No 1 (2019); 30-40 ; Вестник дерматологии и венерологии; Vol 95, No 1 (2019); 30-40 ; 2313-6294 ; 0042-4609 ; 10.25208/0042-4609-2019-95-1
Subject Terms: congenital epidermolysis bullosa, border epidermolysis bullosa, recessive dystrophic epidermolysis bullosa, erosions, healing, external therapy, atraumatic non-adherent wound dressings, врожденный буллезный эпидермолиз, пограничный буллезный эпидермолиз, рецессивный дистрофический буллезный эпидермолиз, эрозии, заживление, наружная терапия, атравматичные неадгезивные перевязочные средства
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Relation: https://vestnikdv.ru/jour/article/view/464/434; https://vestnikdv.ru/jour/article/view/464